Superior semicircular canal dehiscence (SSCD), a bony defect of the arcuate eminence in the middle cranial fossa, is a third-window lesion characterized by sound-induced or pressure-induced dizziness or vertigo. Some patients with SSCD are asymptomatic, and these patients are identified incidentally through computed tomography (CT). However, others experience aural fullness, hyperacusis, transient vertigo, or even chronic disequilibrium. High-resolution CT of the temporal bone is the gold standard for detecting SSCD. Most patients are managed conservatively, but surgery can be offered to patients with symptoms that are debilitating. However, discussing possible postoperative complications with patients is essential. In this paper, we report two cases of SSCD syndrome in patients who underwent repair surgery and their differen presentations and surgical outcomes. (J Taiwan Otolaryngol Head Neck Surg 2022; 57: 227-232)
